Research Paper Volume 12, Issue 17 pp 16690—16708
Metabolic alterations in plasma from patients with familial and idiopathic Parkinson’s disease
- 1 Departamento de Bioquímica y Biología Molecular y Genética. Facultad de Enfermería y Terapia Ocupacional. Universidad de Extremadura, Cáceres, Spain
- 2 Centro de Investigación Biomédica en Red en Enfermedades Neurodegenerativas (CIBERNED), Madrid, Spain
- 3 Instituto Universitario de Investigación Biosanitaria de Extremadura (INUBE), Cáceres, Spain
- 4 Instituto de Investigaciones Biomédicas (CSIC-UAM) “Alberto Sols” (CSIC-UAM), Madrid, Spain
- 5 Departamento de Biología Celular, Facultad de Medicina, Universidad Complutense de Madrid, Madrid, Spain
- 6 Metabolomics and Cell Biology Platforms, Institut Gustave Roussy, Villejuif, France
- 7 Centre de Recherche des Cordeliers, Equipe labellisée par la Ligue contre le cancer, Inserm U1138, Université de Paris, Sorbonne Université, Paris, France
- 8 Cell Culture Platform, Biodonostia Health Research Institute, San Sebastián, Spain
- 9 Neuroscience Area of Biodonostia Health Research Institute, Donostia University Hospital, San Sebastián, Spain
- 10 , Donostia University Hospital, Department of Neurology, OSAKIDETZA, Spain
- 11 Ilundain Foundation, San Sebastian, Spain
- 12 Department of Neurosciences, University of the Basque Country UPV-EHU, San Sebastián, Spain
- 13 Instituto de Biomedicina de Valencia-CSIC, Unidad de Genética Molecular, Valencia, Spain
- 14 Unidad Mixta de Genética y Neurología, Instituto de Investigación Sanitaria La Fe, Valencia, Spain
- 15 , Pôle de Biologie, Hôpital Européen Georges Pompidou, AP-HP, France
- 16 Suzhou Institute for Systems Medicine, Chinese Academy of Medical Sciences, Suzhou, China
- 17 Karolinska Institute, Department of Women's and Children's Health, Karolinska University Hospital, Stockholm, Sweden
- 18 Departamento de Fisiología, Facultad de Medicina, Universidad Complutense de Madrid, Madrid, Spain
Received: June 17, 2020 Accepted: August 15, 2020 Published: September 9, 2020
https://doi.org/10.18632/aging.103992How to Cite
Abstract
The research of new biomarkers for Parkinson’s disease is essential for accurate and precocious diagnosis, as well as for the discovery of new potential disease mechanisms and drug targets. The main objective of this work was to identify metabolic changes that might serve as biomarkers for the diagnosis of this neurodegenerative disorder. For this, we profiled the plasma metabolome from mice with neurotoxin-induced Parkinson’s disease as well as from patients with familial or sporadic Parkinson’s disease. By using mass spectrometry technology, we analyzed the complete metabolome from healthy volunteers compared to patients with idiopathic or familial (carrying the G2019S or R1441G mutations in the LRRK2 gene) Parkinson’s disease, as well as, from mice treated with 6-hydroxydopamine to induce Parkinson disease. Both human and murine Parkinson was accompanied by an increase in plasma levels of unconjugated bile acids (cholic acid, deoxycholic acid and lithocholic acid) and purine base intermediary metabolites, in particular hypoxanthine. The comprehensive metabolomic analysis of plasma from Parkinsonian patients underscores the importance of bile acids and purine metabolism in the pathophysiology of this disease. Therefore, plasma measurements of certain metabolites related to these pathways might contribute to the diagnosis of Parkinson’s Disease.